Project/Area Number |
15K01694
|
Research Category |
Grant-in-Aid for Scientific Research (C)
|
Allocation Type | Multi-year Fund |
Section | 一般 |
Research Field |
Applied health science
|
Research Institution | Nagoya University of Arts and Sciences |
Principal Investigator |
Fujiki Kotoyo 名古屋学芸大学, 管理栄養学部, 教授 (50454450)
|
Research Collaborator |
ISHIGURO Hiroshi 名古屋大学, 総合保健体育科学センター, 教授 (90303651)
|
Project Period (FY) |
2015-04-01 – 2018-03-31
|
Project Status |
Completed (Fiscal Year 2017)
|
Budget Amount *help |
¥4,940,000 (Direct Cost: ¥3,800,000、Indirect Cost: ¥1,140,000)
Fiscal Year 2017: ¥650,000 (Direct Cost: ¥500,000、Indirect Cost: ¥150,000)
Fiscal Year 2016: ¥910,000 (Direct Cost: ¥700,000、Indirect Cost: ¥210,000)
Fiscal Year 2015: ¥3,380,000 (Direct Cost: ¥2,600,000、Indirect Cost: ¥780,000)
|
Keywords | 栄養指導 / 栄養管理 / 膵嚢胞線維症 / 難治性希少疾患 / 低栄養 / 栄養管理法の確立 / 嚢胞性線維症 / CFTR遺伝子変異 / 膵外分泌不全 / 患者家族会 / 栄養管理法 / 難治性膵疾患 / CF登録制度 / 栄養評価 |
Outline of Final Research Achievements |
Cystic fibrosis (CF) is an autosomal recessive disease caused by mutations in CFTR. Although CF is the most common hereditary disease in Caucasians, it is rare in Asian populations. Pancreatic insufficiency remains a significant issue for the majority of individuals with cystic fibrosis. Nutritional support is a vital component of care for patients. We established the Nutrition Care Guidelines for Japanese patients with CF. This Guidelines cover caloric intake, dosing for pancreatic enzyme replacement therapy, monitoring growth, and weight control in patients.
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